著者
Seigo Okada Jun Muneuchi Yusaku Nagatomo Kaori Nonaka Chiaki Iida Hiromitsu Shirouzu Ryohei Matsuoka Mamie Watanabe Kunitaka Joo
出版者
International Heart Journal Association
雑誌
International Heart Journal (ISSN:13492365)
巻号頁・発行日
vol.59, no.4, pp.873-876, 2018-07-31 (Released:2018-07-31)
参考文献数
11
被引用文献数
6 7

We present a 16-year-old male patient with hypoplastic left heart syndrome who developed protein-losing enteropathy (PLE) and plastic bronchitis (PB) after a Fontan operation. He received medical therapies, including albumin infusion, unfractionated heparin, and high-dose anti-aldosterone therapy but could not obtain clinical relief. Biphasic cuirass ventilation (BCV) led to expectoration of bronchial casts and prompt resolution of PB. Notably, clinical symptoms related to PLE were dramatically improved after starting BCV. A brief period of BCV increased stroke volume from 26±1.4 to 39±4.0 mL. This case suggests that BCV could be an effective treatment for PLE in patients with failing Fontan circulation.

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@josephspinner @angie_lorts @mgoschu @AriCedars @DukeHFDoc @RyanTedfordMD Advanced #ironlung for negative pressure ventilation would be a more practical option https://t.co/pav3WjWlBE

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