著者

Noriko OHARA Ichiro KOMIYA Keishi YAMAUCHI Hiromi OHTSUKA Yoshitaka NAGASAWA Teiji TAKEDA Nobuyuki TAKASU

出版者

一般社団法人 日本内科学会

雑誌

Internal Medicine (ISSN:09182918)

巻号頁・発行日

vol.32, no.1, pp.60-62, 1993 (Released:2006-03-27)

参考文献数

9

被引用文献数

4 7

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Carney's complex is composed of myxoma, spotty pigmentation and endocrine overactivity. A 27-year-old male was diagnosed to have Carney's complex on the basis of intense spotty pigmentations on his face, soles and palms, and bilateral adrenal nodular hyperplasia on computed tomography scanning (CT) and magnetic resonance imaging (MRI). Total bilateral adrenectomy was done; histological findings were compatible with primary pigmented adrenocortical disease (PPNAD). Recently, his sister and one of his brothers were suspected to have Carney's complex with PPNAD. We report the first familial case of Carney's complex with PPNAD and spotty pigmentations in Japan.(Internal Medicine 32: 60-62, 1993)