著者
Kazuhiro Koyanagawa Yuta Kobayashi Tadao Aikawa Atsuhito Takeda Hideaki Shiraishi Satonori Tsuneta Noriko Oyama-Manabe Hiroyuki Iwano Toshiyuki Nagai Toshihisa Anzai
出版者
Japanese Society for Magnetic Resonance in Medicine
雑誌
Magnetic Resonance in Medical Sciences (ISSN:13473182)
巻号頁・発行日
pp.bc.2020-0069, (Released:2020-09-07)
参考文献数
18
被引用文献数
1

To assess myocardial fibrosis associated with muscular dystrophy, T1-mapping and extracellular volume fraction (ECV) quantification was prospectively performed using cardiovascular MR (CMR) imaging in 6 male patients with muscular dystrophy and 5 female putative carriers of Duchenne or Becker muscular dystrophy. Five patients and all putative carriers had an elevated ECV (>29.5% for men and >35.2% for women), suggesting that ECV has a potential to detect diffuse fibrotic changes in patients and putative carriers of muscular dystrophy.

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心移植の原因ともなり得る筋ジスの二次性心筋症。実は保因者もMRIを撮ったら所見があったり、心機能低下症例もいます、という我々からの報告です https://t.co/zZv0rRIJZ2

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