著者

川口 忠恭 謝花 幸祐 岡本 奈美 稲毛 康司

出版者

一般社団法人 日本小児リウマチ学会

雑誌

小児リウマチ (ISSN:24351105)

巻号頁・発行日

vol.11, no.1, pp.30-35, 2020 (Released:2021-10-06)

参考文献数

22

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Anti-Mi-2 antibody-positive juvenile dermatomyositis(JDM) is considered as a good prognostic inflammatory myositis for which steroid drug is effective. Although it is relatively rare in Japanese JDM, and it is also clarified that a steroid-resistant and intractable phenotype is occasionally present by our report. In such patients with steroid-resistant anti-Mi-2 antibody-positive JDM, we conclude that IVIG might be useful as a second-line drug.