著者

中江 進 水田 康雄 八木 美知 平杉 嘉昭 水越 治

出版者

The Society of Practical Otolaryngology

雑誌

耳鼻咽喉科臨床 (ISSN:00326313)

巻号頁・発行日

vol.72, no.11, pp.1469-1477, 1979

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Five patients with a congenital deafness caused by maternal rubella infection during pregnancy visited our clinic in 1977. The ages ranged from 3 to 11 months. The diagnosis of deafness was made mainly by Brain Stem Response, partly startle response and C. O. R.<br>Case 1 was diagnosed as a typical congenital rubella syndrome, because of the high HI titer, congenital deafness, PDA+ASD, retinochoroidal degeneration, thrombocytopenia, and hepatosplenomegaly. Case 4 whose HI titer was high was accompanied by microphthalamia and anophthalamia with a positive response at 40dBSL in BSR the left ear and 50dBSL in the right ear.<br>We conclude that congenital deafness should be determined by Brain Stem Response as early as possible so that an early diagnosis of hearing impairment can be made.