著者
濱谷 美緒 陣上 直人 植村 健吾 仲宗根 眞恵 木下 久徳 山門 穂高 二宮 治明 髙橋 良輔
出版者
日本神経学会
雑誌
臨床神経学 (ISSN:0009918X)
巻号頁・発行日
vol.56, no.6, pp.424-429, 2016 (Released:2016-06-22)
参考文献数
19

症例は40歳男性.新生児期に遷延性黄疸を認めた.幼少時に自閉症が判明し,カレンダー計算能力をもちsavant症候群を合併した.15歳に幻視と幻聴を認め,30代後半から垂直方向の核上性注視麻痺,四肢脱力発作,小脳失調を認めた.臨床像からニーマン・ピック病C型(Niemann-Pick disease type C; NPC)を疑い,培養皮膚線維芽細胞のfilipin染色からNPCのvariant biochemical phenotypeと考えた.成人期発症のNPCは精神神経症状が主体となり,相対的に症状が軽いvariant biochemical phenotypeを呈することが多いとされ,診断は困難である.NPCは皮膚生検と遺伝子検査により診断可能であり,近年本邦でも治療薬が承認されているため,特徴的な臨床症状を呈する場合は検索を行うことが重要である.

2 0 0 0 OA 岩永随筆 5巻

出版者
巻号頁・発行日
vol.[3],
著者
木村 友子 福谷 洋子 菅原 龍幸 佐々木 弘子
出版者
一般社団法人 日本調理科学会
雑誌
日本調理科学会誌 (ISSN:13411535)
巻号頁・発行日
vol.28, no.1, pp.24-31, 1995-02-20 (Released:2013-04-26)
参考文献数
11

To develop a new cooking method for rapid rehydration of dried radish (strips of dried radish), several conditions for rehydration including a step of ultrasono-irradiation were studied. The conditions for the best rehydration were determined at 5,25 and 40°C and the effects of ultrasonication on physical properties and palatability of the cooked radish were investigated. The results were as follows:(1) The amount of water absorbed into dried radish increased as the rehydration time goes up. The irradiated radish showed further improved swelling in shorter time and their tissues were softened faster than those in the control without irradiation.(2) When rehydration was conducted under the suitable conditions at the water temperature of 25°C, no difference was observed between the subjects irradiated for 15 min and those soaked for 30 min without irradiation, with regard to in the contents of moisture, total sugar, free sugar, crude protein, free amino acids and ashes, and the remaining proportions of mineral components in both subjects were 81% for Ca,70% for iron and 69% or more for Mg.(3) For texture characteristics, ultrasono-irradiated radish after cooking exhibited large rupture strain and chewiness than the control without irradiation. In addition, the permeability of seasonings was a little higher in ultrasono-irradiated radish and also the odor specific to the dried radish was somewhat decreased, resulting in superior taste evaluation.
出版者
財界21
巻号頁・発行日
vol.夏季特集12, no.8, 1983-08

2 0 0 0 OA 祝の書

著者
伊勢貞丈 述
出版者
市川熊男 写
巻号頁・発行日
1843
著者
山口 孝夫 岩田 英敏
出版者
大同特殊鋼株式会社
雑誌
電気製鋼 (ISSN:00118389)
巻号頁・発行日
vol.75, no.4, pp.297-303, 2004-10-15 (Released:2010-06-02)
参考文献数
9

In recent years, SQUID (superconducting quantum interference device) technology has been developed for measuring the very low magnetic field generated from a human's physiology activity, and this technology is used for MEG (magnetencephalograph) and MCG (magnetcardiograph). In this way, the MEG and MCG have begun to be installed to the some hospitals as the medical devices. It is necessary to reduce the environmental magnetic field significantly, in order to measure the weak signals with high stability by using these devices. We developed and manufactured the magnetic shielding room for this purpose. In this paper, shielding performance of the magnetic shielding room at the low intensity and low frequency magnetic field is introduced.
著者
柳亭種彦 作
出版者
鶴屋喜右衛門
巻号頁・発行日
vol.弐編, 1828

2 0 0 0 OA 以呂波抄

著者
如得 [著]
巻号頁・発行日
1761
著者
並木五瓶 作
出版者
森屋治郎兵衛
巻号頁・発行日
1849

2 0 0 0 OA いろはうた

著者
辻慶儀 著
出版者
[出版者不明]
巻号頁・発行日
1844
著者
為永春水二世 作
出版者
巻号頁・発行日
vol.[9],